ISSN: 1300-0292 İndekslendiği Dizinler: SCIENCE CITATION INDEX EXPANDED CINAHL, Index Copernicus, Chemical Abstracts (CA), Excerpta Medica / EMBASE Dil: Türkçe, İngilizce İçerik: Orijinal Araştırma, Derleme, Editöre Mektup, Olgu Sunumu, Tıp Eğitimi, Tıbbi Kitap İncelemeleri
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Linear Iga Bullous Dermatosis Associated With Iga Nephropathy: Case Report
Dr. Fidan YEGİN,a Dr. Güler VAHABOĞLU,a Dr. Meral EKŞİOĞLU,a Dr. Murat DURANAY,bDr. Nilüfer ARDA,c Dr. Dilek ERTOY BAYDAR,d Dr. Muzaffer ÇAYDEREe
aDermatoloji Kliniği, bbNefroloji Kliniği, Ankara Eğitim ve Araştırma Hastanesi,cPatoloji Kliniği, Dr. Sami Ulus Çocuk Hastanesi,dPatoloji AD, Hacettepe Üniversitesi Tıp Fakültesi,ePatoloji Kliniği, Ankara Eğitim ve Araştırma Hastanesi, ANKARA Linear IgA bullous dermatosis is a rare autoimmune disease characterized by subepidermal blister formation and linear IgA deposition in the dermoepidermal junction. Linear IgA bullous dermatosis seems to be associated with several chronic diseases. Five cases with concurrent glomerulonephritis and linear IgA bullous dermatosis were reported. Although an autoantibody against the basal membrane was detected, but exact pathological mechanism is still unclear. We present a case with concurrent linear IgA bullous dermatosis and IgA nephropathy and discuss the correlation between the two conditions using recent data.Keywords: Skin diseases; immunoglobulin A; glomerulonephritis; IGATurkiye Klinikleri J Med Sci 2007, 27:124-127
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